An infant with massive haemobilia due to cavernous transformation of the portal vein.
نویسندگان
چکیده
Haemobilia or bleeding into the biliary tract is a very rare occurrence in children. We report an infant who bled profusely into the biliary tract from dilated pericholecystic veins that were part of a sponge like mass of tortuous, collateral veins replacing the portal vein. This venous anomaly is referred to as cavernous transformation of the portal vein or portal cavernoma and is a sequel of portal vein thrombosis [1,2].
منابع مشابه
Thrombotic microangiopathy and fibrinolysis after hump-nosed viper envenomation.
Massive haemobilia due to rupture of a portal cavernoma is very rare. In our patient the cause for portal vein thrombosis remains obscure in the absence of umbilical sepsis, severe dehydration or a hypercoaguable state. Cavernous transformation has been documented even within a few days of the portal vein getting obstructed; and inflammation resulting from enteritis is a recognised cause of por...
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Cavernous transformation of portal vein consists in the development of a network of tortuous collateral vessels bypassing the obstructive area due to chronic PVT. First described in 1869 by Balfour and Stewart, it was Köbrich in 1928 that used for the first time the term of “cavernoma” to define the newly developed network of small vessels as a result of recanalization of the thrombotic portal ...
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Cavernous transformation is a condition which has an acutely developing harmful effect over intestinal circulation compromising the patients' life before development of portal hypertension and its results. We present the case of phrenic artery hemorrhage after successful percutaneous portal vein stenting to treat cavernous transformation following LDLT. The patient survived the hazard complicat...
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ورودعنوان ژورنال:
- The Ceylon medical journal
دوره 57 1 شماره
صفحات -
تاریخ انتشار 2012